This condition of general weakness and fatique is associated with thymoma
Myasthenia Gravis
In this phenomenon, increased CMAP amplitudes are seen with repetitive stimulation (after subsequent stimulation) due to better SYNCHRONY of muscle fibers action potentials.
Pseudofacilitation
This substance can cause Descending weakness ( CN muscles-> shoulders->feet).
Botulinum toxin
This condition is caused by deficiency in ACH storage, mobilization, re-synthesis and as muscle weakness in NEWBORN.
Congenital Myasthenia
Which NMJ is associated with dry mouth, metallic taste, constipation, erectile dysfunction?
Eaton-Lamberg Syndrome
Which NMJ condition is associated with reduced MEPP amplitudes?
Myasthenia Gravis
What % is considered significant?
10% decrement
This condition is characterized by antibodies against voltage gated Ca++ channels in the NMJ.
Eaton Lamberg Syndrome
In this condition, antibodies block ACH receptors at postsynaptic neuromuscular junction of skeletal muscles
Myasthenia Gravis
In this condition, ACHesterase inhibitor (Edrophonium) reverses weakness.
Myasthenia Gravis
This term is defined as the VARIABILITY of potential time between 2 action potentials from 2 muscle fibers belonging to the same unit.
Jitter
Which NMJ condition is associated with very low CMAP amplitude on NCS?
Eaton-Lamberg Myasthenic syndrome
This phenomenon occurs after high rates of stimulation (20-50HZ) or tetanic contraction
Post-tetanic facilitation or potentiation
Which NMJ disorder usually spares bulbar and extraoccular muscles?
Eaton-Lamberg Syndrome
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