Which motor neuron lesion (upper, lower, central) is affected by marked muscle wasting and atrophy, Flaccid hypotonic muscles, Diminished or absent DTRs, Muscle cramps Fasciculations
lOWER MOTOR NEURON LESION
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20
Which of the following are NOT a usual electrodiagnostic fining in ALS?ย A. Tongue fasculation,B. PSW in thoracic paraspinals,C. absent right tibial motor NCS, D. absent left sural NCS
Absent left sural nerve
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20
What tract does ALS affect ( be specific)
Lateral Corticospinal tract
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20
Which condition is often confused with Progressive Muscle Atrophy(PMA) , Predominant LMN symptoms, slowly progressive ; 2:1 (M:F); onset before 5th decade Progressive, asymmetric weakness, often of distal UE first
Multifocal Motor neuropathy
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20
Which of the following EMG/NCS findings can help predict prognosis? PSW in FDI, reduced CMAP in tibial, absent ulnar study, fasciculations in gastroc.
reduced CMAP amplitude
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Where are the Anterior Horn cells
B
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20
Which condition affects: Both UMNs + LMNs,ย onset later in life,ย Spares sensory, vision, hearing and autonomic functions, Intactย Cognition ?
ALS
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20
Which variant of ALS presents initally with bulbar symptoms (Dysarthria, drooling, gagging, dysphagia, choking) and โhandkerchief signโ?
progressive bulbar palsy
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20
Which condition starts in one limb,ย spreads to adjacent myotomes and eventually spread to contralateral limb, then bulbar, and respiratory muscles?
ALS
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How does Kennedy's disease ( SMA) differ from ALS on NCS testing?ย ย Kennedy's dz has reduced SNAP amplitude, Kennedy's affects mostly female, Kennedy's presents in children :
Kennedy's disease presents with low amplitude SNAPs due to DRG involvement
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Which ALS Variant presents with Pure LMN symptoms, distal limb wasting and weakness, fasciculations, cramps, reduced reflexes in weak limbs long clinical course, slow progression to prox limb muscles. No sensory symptoms